TOTBİD Dergisi

TOTBİD Dergisi

2016, Cilt 15, Sayı, 4     (Sayfalar: 279-287)

Evaluating lower extremity deformities in skeletal dysplasias

Ozan Ali Erdal 1, Muharrem İnan 2

1 Ortopediatri, İstanbul
2 İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Ortopedi ve Travmatoloji Anabilim Dalı, İstanbul

DOI: 10.14292/totbid.dergisi.2016.34
Görüntüleme: 764
İndirme : 2249

Lower extremity deformities causing decrease in quality of life are commonly seen in patients with skeletal dysplasia. Although some deformities are seen more frequently in specific types of dysplasia, deformities commonly arise from asymmetrical involvement of physes, different longitudinal growth rates of tibia and fibula in the leg, contractures around the joints or joint instabilities due to ligamentous instability. The most common deformities of lower extremities in skeletal dysplasias are coxa vara, coxa valga, genu varum, genu valgum and ankle valgus or varus. When starting to deal with these deformities surgeon should primarily be familiar with general deformity treatment principles. In different studies different treatment protocols are supported for deformities in skeletal dysplasias. Selection out of different correction choices can be done considering clinical condition, future growth potential, magnitude of dwarfism of the patient and characteristic phenotype of a definite dysplasia. Correction can be achieved by either acute correction methods or gradual correction with hemiepiphysiodesis or external fixator systems. Because of lack of definite growth presumption in these patients, sometimes inadequate corrections happen. Also, sometimes a thoroughly corrected deformity might recur in a growing child with skeletal dysplasia.

Anahtar Kelimeler : skeletal dysplasia; genu varum; genu valgum; coxa vara; coxa valga; deformity correction